Congenital malignant gliosarcoma.

Malignant gliosarcoma is an extremely rare, anaplastic tumor which to date has been found exclusively in adults. This type of sarcoma is a form of mixed glioma and sarcoma which is quite different and distinct from the type of sarcoma that arises in a glioblastoma [1]. Less than 10 cases of this entity have been reported [2-5]. We report a case of this unusual tumor in a 4-month-old girl who had lethargy and macrocephaly. Although the clinical, radiographic, and angiographic manifestations of intracranial sarcomas have been described [1-10], the computed tomographic appearance of a primary malignant gliosarcoma has not been published.